Endocrine

VIPoma

Also known as Verner-Morrison syndrome, pancreatic cholera, WDHA syndrome, vasoactive intestinal peptide tumor

VIPoma is a rare pancreatic or extra-pancreatic neuroendocrine tumour that secretes excess vasoactive intestinal peptide (VIP), causing a distinctive syndrome of profuse watery diarrhoea, hypokalaemia, and achlorhydria collectively termed W

ORPHA:525 ↗Prevalence Less than 1 per million per yearOnset Most commonly in adults aged 40–60Sporadic (majority); rarely associated with MEN1

0

studies recruiting now

as of 7 Sept 2026

23

studies registered in total

as of 7 Sept 2026

0

countries with a recruiting site

as of 7 Sept 2026

None

recruiting study posted to date

among recruiting studies

Recruiting trials

No recruiting trial found right now.

23 studies are registered for VIPoma, but none was recruiting as of 7 Sept 2026. Here is what is still worth doing.

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About VIPoma

VIPoma is a rare pancreatic or extra-pancreatic neuroendocrine tumour that secretes excess vasoactive intestinal peptide (VIP), causing a distinctive syndrome of profuse watery diarrhoea, hypokalaemia, and achlorhydria collectively termed WDHA syndrome or Verner-Morrison syndrome. The massive secretory diarrhoea, which persists even with fasting, leads to severe electrolyte disturbances, dehydration, and metabolic acidosis that can be life-threatening if untreated. Over 50% of VIPomas are malignant at the time of diagnosis, with liver metastases commonly present, making systemic therapy trials particularly relevant for this tumour type.

Common clinical features

Profuse watery diarrhoea (3–5 litres or more per day)Severe hypokalaemiaAchlorhydria or hypochlorhydriaDehydration and weaknessFlushing episodesHyperglycaemiaHypercalcaemiaWeight loss and malnutrition

From Orphanet’s phenotype annotations (CC BY 4.0). Not a complete list.

Before you apply

Things trial teams commonly ask about for VIPoma. Not eligibility rules; those are set by each study.

  • Elevated fasting plasma VIP level (typically greater than 200 pg/mL) combined with characteristic symptoms and imaging evidence of a pancreatic or retroperitoneal mass is required for trial eligibility confirmation.
  • Correction of electrolyte abnormalities (particularly hypokalaemia) to safe levels before screening is a standard requirement; recent electrolyte results and repletion history should be documented.
  • Functional imaging with 68Ga-DOTATATE PET or octreotide scan assessing somatostatin receptor expression is required for trials of somatostatin analogues or PRRT; receptor positivity is often an eligibility criterion.

Related conditions

Information, not medical advice. Trial listings are shown as recorded on ClinicalTrials.gov; whether any study is right for you is a decision for you and your clinicians, and eligibility is decided by each research team. Disease information from Orphanet (CC BY 4.0).