Neurological

Neuroacanthocytosis

Also known as Chorea-acanthocytosis, McLeod syndrome, VPS13A deficiency, XK protein deficiency

Neuroacanthocytosis syndromes are a group of rare genetic disorders characterized by progressive neurodegeneration with movement disorder and acanthocytes (spiked red blood cells) on peripheral blood smear. The two main forms are chorea-aca

ORPHA:2388 ↗Gene VPS13A (chorea-acanthocytosis)Gene XK (McLeod syndrome)Prevalence 1-9 per 1,000,000 (Orphanet)Onset Adolescent, AdultAutosomal recessive (chorea-acanthocytosis) or X-linked (McLeod syndrome)

0

studies recruiting now

as of 7 Sept 2026

1

studies registered in total

as of 7 Sept 2026

0

countries with a recruiting site

as of 7 Sept 2026

None

recruiting study posted to date

among recruiting studies

Recruiting trials

No recruiting trial found right now.

1 study is registered for Neuroacanthocytosis, but none was recruiting as of 7 Sept 2026. Here is what is still worth doing.

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About Neuroacanthocytosis

Neuroacanthocytosis syndromes are a group of rare genetic disorders characterized by progressive neurodegeneration with movement disorder and acanthocytes (spiked red blood cells) on peripheral blood smear. The two main forms are chorea-acanthocytosis (VPS13A mutations, autosomal recessive) and McLeod syndrome (XK mutations, X-linked). Features include orofacial dyskinesia, self-mutilation, chorea, parkinsonism, cognitive decline, epilepsy, cardiomyopathy, and elevated serum creatine kinase.

Common clinical features

Orofacial dyskinesiaChoreaSelf-mutilating lip and tongue bitingAcanthocytosis on blood smearElevated serum creatine kinaseCognitive declineSeizures

From Orphanet’s phenotype annotations (CC BY 4.0). Not a complete list.

Before you apply

Things trial teams commonly ask about for Neuroacanthocytosis. Not eligibility rules; those are set by each study.

  • Peripheral blood smear confirming acanthocytes (>3% in context of clinical features) is a required diagnostic marker
  • Specify neuroacanthocytosis form — VPS13A (chorea-acanthocytosis) versus XK (McLeod syndrome) have distinct genetics and trial eligibility
  • For McLeod syndrome: Kell antigen blood group phenotyping is a critical safety marker — blood transfusion history must be documented
  • Creatine kinase, liver enzymes, and cardiac evaluation (ECG, echocardiogram) are required baseline safety and eligibility assessments

Related conditions

Information, not medical advice. Trial listings are shown as recorded on ClinicalTrials.gov; whether any study is right for you is a decision for you and your clinicians, and eligibility is decided by each research team. Disease information from Orphanet (CC BY 4.0).